Headache caused by but not usually a presenting or prominent symptom of any of a variety of autoimmune disorders, and associated with other symptoms and/or clinical signs of the causative disorder. It remits after successful treatment of the autoimmune disorder.
- Any headache fulfilling criterion C
- A non-infectious inflammatory disease known to be able to cause headache, other than those described above, has been diagnosed1
- Evidence of causation demonstrated by one or more of the following:
- headache has developed in temporal relation to the onset of the non-infectious inflammatory disease
- headache has significantly worsened in parallel with worsening of the non-infectious inflammatory disease
- headache has significantly improved in parallel with improvement in the non-infectious inflammatory disease
- Not better accounted for by another ICHD-3 diagnosis.
Headache can be causally associated with, but is not usually a presenting or prominent symptom of, acute demyelinating encephalomyelitis (ADEM), systemic lupus erythematosus (SLE), Behçet’s syndrome and other systemic or focal (eg, limbic encephalitis) autoimmune syndromes.