Migraine-like attacks, with or without aura, caused by and occurring as part of the clinical manifestations of a genetic or non-genetic chronic intracranial vasculopathy other than those described above.
- Recurrent migraine-like attacks, with or without aura, fulfilling criterion C
- A genetic or non-genetic chronic intracranial vasculopathy has been demonstrated
- Migraine-like attacks are secondary to and part of the clinical manifestations of the chronic intracranial vasculopathy
- Not better accounted for by another ICHD-3 diagnosis.
Recurrent migraine-like attacks have been reported as part of the clinical manifestations of the autosomal dominant hereditary infantile hemiparesis, retinal arterial tortuosity and leucoencephalopathy (HIHRATL), a condition due to COL4A1 mutations. Only a few families with this disorder have been reported. Because of the other severe manifestations, these migraine-like attacks have not been systematically investigated in HIHRATL but they appear mainly to resemble 1.2 Migraine with aura.
All of the other rare genetic and non-genetic chronic intracranial vasculopathies can, potentially, cause migraine-like attacks.