Headache and/or pain in the face and/or neck caused by non-inflammatory lesions affecting the cervical carotid and/or vertebral arteries. The pain generally has a sudden (even thunderclap) onset. It can remain isolated or be a warning symptom preceding the focal deficits of ischaemic stroke.

Diagnostic criteria:
  1. Any new headache and/or facial or neck pain fulfilling criterion C
  2. A cervical artery lesion has been demonstrated, or a surgical or radiological intervention has been performed on a cervical artery
  3. Evidence of causation demonstrated by at least two of the following:
    1. pain has developed in close temporal relation to other local signs of a cervical artery disorder, or has led to the diagnosis of a cervical artery disorder
    2. either or both of the following:
      • a) pain has significantly worsened in parallel with other signs of the cervical artery lesion
      • b) pain has significantly improved or resolved within 1 month of its onset
    3. pain is unilateral and ipsilateral to the affected cervical artery
  4. Not better accounted for by another ICHD-3 diagnosis.